Figure 2

Patient 2. a. Pure-tone audiometry: moderate sensorineural hearing loss on the right and moderate mixed conductive-sensorineural hearing loss on the left. b. Stabilometry: body swaying with her eyes open. c. Nystagmus test: horizontal nystagmus to the right during the supine roll test. d. VEMP: bilateral absent. e. MRI: T2*-weighted images revealed hemosiderosis around the brainstem and the cerebellum, partially the lateral Sylvian fissure and longitudinal cerebral fissure (arrow).